My Carcinoid Story

by

Bill Evans

You may contact Bill via email   billmargie@comcast.net

 

June 2003

My experience with Carcinoid Syndrome began in January 1995 although I did not know it at the time.  It was late in the month when the wife and I went to a local hardware store to purchase a furnace filter.  Overcome by a very strange sensation I asked Margie if she could smell something “strange”.  She replied no and asked me what it smelled like.  I could not identify the smell or for that matter if it really was a smell… more like a burning sensation in my nose, throat and chest. 

 

After a few moments it passed and we proceeded to search for the filters.  About 60 seconds later it hit me hard.  I had no idea what was going on.  I only knew I was sick and needed to do something about it right now.  We left the store and the wife drove us to a nearby hospital where upon a brief examination in the parking lot they determined I was having a heart attack!  And so I was.  They lost me for a short while but when I awoke it began a very long day of treatment followed by surgical procedures and medications.

 

It is because of the medications that my primary physician and I were thrown off the track about symptoms we now recognize are related to Carcinoid Syndrome.  The doctor expressed the opinion that my flushing and diarrhea were related to undesired but not unexpected effects of heart medications. 

 

Twice a year I visited with the primary care physician and once a year visited the heart doctor for tests.  Each time I was pronounced as being in extremely good shape… for a man my age and medical history.  In fact at 59 I was told I could outdo most 40 year old men on the treadmill.

 

At each of these visits and those occasions I had a cold or some problem that sent me to the doctor’s office I brought up the matter of increasing incidences of flushing and diarrhea.  Each time I was told the same thing, reaction to the medications.  And so it went until March 2002.  Yes, seven years later!

 

By March 2002 the diarrhea had advanced to the point that it was socially embarrassing which prompted an “early retirement” and I did not leave my home office very often.  Taking meals with business associates and friends had been dwindling due to the embarrassing flushing events when my neck, face and head became extremely red and always created comments at the table.

 

But now I was becoming weak, listless and apathetic.  I had started a consulting business to work out of my home office during hours I wanted and doing the kind of work I wanted to do.  Even with that freedom, I just didn’t feel like doing anything and the symptoms got worse.

 

In May I knew something was terribly wrong and that after all this time my doctors could not or would not even look into the possibility of something else causing my problems.  So I contacted the Sansum Clinic in Santa Barbara and made an appointment for a complete examination.  During the initial interview the physician narrowed down my problem to one of three possibilities and ordered tests to isolate the cause of my distress. 

 

The tests indicated it was the worst possible cause, Carcinoid Syndrome.  Of course we had no idea what that was but the doctor explained the condition was consistent with my symptoms.  It wasn’t until about the fourth or fifth meeting with the doctor that week that he used the dreaded “C” word, cancer.  I still recall the shock of hearing it for the first time as it related to my condition.  We had been discussing the possibility of a tumor but this was the first time it was suggested it was other than benign.

 

They recommended surgery and we took that under advisement as we returned to our home to consider all the options.  During the next several days the pain grew worse each time I would eat and create “movement” in the intestines.  The main cancer mass and tumor was located at the point where the small intestine meets the colon and it failed to show on all tests with the exception of a CT scan.  This scan also showed that the liver was fully involved with over 20 tumors.

 

We accepted the doctor’s recommendation for surgery and in late August 2002 a considerable amount of my internal parts were removed.  A biopsy of these parts revealed cancer was involved in each one.  The tumors in the liver were to far advanced for surgical procedures.  For the first time we learned that this was incurable and inoperable. 

 

The only good news was it was a “slow growing” cancer.  I asked what that meant.  Did that mean I got to live longer with the problem?  Take longer to die than those with “fast growing” cancer?  Why can’t it be operated on?  Why isn’t it curable?  And many more questions that all support the denial portion of my journey.  This passed quickly but it was still a shock.

 

I began a regimen of LAR injections of Sandostatin for the Carcinoid Syndrome in November 2002, and Testosterone for physical weakness in February 2003.  I understood that in time the liver might build up antibodies to the medication and reduce its effectiveness.  In the beginning to intermediate stages this can sometimes be estimated but in advanced cases such as mine, well, no one knows.  We all take it one day at a time.

 

Statistically, life expectancy from the onset of symptoms has been stated around 7.42 years.  Just about the same amount of time the doctors ignored my symptoms and complaints.  It has been over 8 years and although my case is in an advanced stage, I am still here and able to function.  OK, not like before but then I am not confined to 30 paces from my toilet.  I eat a lot of things I simply could not before the surgery and medications, and that is a big improvement.

 

I have avoided documenting the details and statistics of my journey with Carcinoid Syndrome since every case seems to be as unique as the individual.  What we are all interested in is what will happen next.  Will there be pain?  How long do I have?  No one is comfortable discussing these issues but yet that is what we all want to know. 

 

Here is the answer; but I warn you, it is not very satisfying.  It differs for each person.  Your journey is just that, your journey.  The end of your life is as unique as how you lived it.  Not everyone lives exactly the same or passes the same.  How is will end for others is not necessarily how it will end for you.

 

When I was born, 65 was the life expectancy for most children in the United States.  So that number has had a special meaning for me all throughout my life.  My Dad died at age 55, just before his 56th birthday and I wondered if I would make it to my “allotted” time.  God has been good and I indeed did make it to 65.

 

It may be important to point out that maintaining a positive attitude is very helpful.  There is always hope.  Hope for a cure, a significant delay, a reversal, anything that will help you feel better.  Yet we all know that someday this life’s journey will come to a close.  Don’t let the illness defeat you.  It is a major problem but your whole life is not the Syndrome.  It is just one of the many things you have to deal with and you have dealt with a lot of other issues in your life.  So kept on keeping on.

 

Believing that every life story should have a moral, or at least a purpose, here is my encouragement to anyone reading this and trying to learn more about Carcinoid Syndrome.

 

Take responsibility for your own body!  Doctors are very much like any other profession.  They can advise but it is YOU that must decide!  They are busy doing a fantastic job for the most part and society is and should be indebted to those in this profession.  But, they are not perfect and given their case loads, insurance companies, government regulations, etc. they do a wonderful job.  Only you know your body and how you feel.  Don’t accept fast answers if it just doesn’t seem right.  Get another opinion.

 

Don’t wait to long!  If I had acted upon my condition a few years before I did, I might have a good chance of extending my life expectancy not to mention the quality of life.  (And keep my innards).

 

Don’t let the condition dominate your entire life.  As long as you are still alive, live! 

 

Do not accept defeat.  Only you can let yourself be defeated.

 

When I learned about my condition I wrote the attachment and during the past several months my opinion has not wavered.  If you find some comfort from this then please use it to your best advantage.

 

May God continue to bless and keep you and yours.

Bill Evans

 

September 25, 2003

Update:  As expected the medication has been compromised.  A recent CT scan revealed that the tumors are growing again.  Pain has become a 24/7 situation.  Usually it is just darn uncomfortable but then about once a day, the pain hits incredibly hard.  Bad enough to send me to my knees crying.  The doctor has increased my medication to a 30 gram shot of LAR every two weeks.  He plans to start chemo in perhaps October.

 

February 20, 2004

The latest CT Scan shows that 5 of the tumors have grown together and represent a mass that measures 7 X 5 X 4 cm, about the size of a large avocado.  The second largest mass is just a little smaller.  There are still numerous small tumors.  I am receiving the maximum amount of LAR every two weeks, the minimum time frame, and there are continuing and increasing signs the medication has been compromised.  It can only get worse.

 

I am on my fourth chemo treatment which is administered 24 hours a day for 5 days.  Then a rest for 23 days and start over.  It makes me sick and weak but the doctor seems to think it is helping.  There is no clear evidence that is the case.  Each time I have this treatment I must drive 100 miles round trip and 3 times during the treatment period.  This is proving to be a burden so I am looking for another doctor in my town that is familiar with Carcinoid Syndrome treatments.

 

I wrote to the two US Senators and 5 of the US Representatives that I know personally and requested their assistance in obtaining the “Rotterdam” treatment for patients in the US.  We want the FDA to move things along.  They are working the case and we hope to have word soon.

 

September 2004

Well, we heard back from the elected officials and learned that the FDA does not seek out drug therapies to approve.  They must wait until the drug and its data is submitted before they can take action.  The drug company has not finished their studies and not submitted any requests to the FDA for approval.  So much for that course of action.

 

The LAR continued to decline in effectiveness and usually “wear off” about 7 to 10 days after the injection.  That leaves about 4 to 6 days every two weeks where there is minimum relief from the LAR.

 

With the kind assistance of my new Oncologist, who is located in my same town and much easier to access, we stopped the chemo, which was not apparently helping in any manner, and found a clinical trial at UCLA in Los Angeles that might help my condition. 

 

Went to UCLA and found a wonderful group of dedicated professionals that were very helpful.  However, their trial was not appropriate for my condition.  Most of the trials I looked at had a list of conditions that one must meet before they can be accepted.  Like age, sex, previous health events, current condition of the disease, etc.  I was not eligible for any of them.

 

When we returned from the UCLA trip I was feeling somewhat hopeless.  It was one of those, “Now what do we do?” times.  Then by chance, or divine guidance, I went online to http://clinicaltrials.gov/ and learned of a program being conducted at Cedars-Sinai in Los Angeles.  I couldn’t believe it!  It was if it were written exactly for my condition.  So I called, they sent material via e-mail.  I wrote back, they called and set an appointment.

 

On August 16, 2004 we met with Dr. Stephen Lim and were accepted into the study.  It is a test of a new drug termed SOM230 and it uses four of the five Human Somatostatin Receptor Subtypes, (HSSTS) instead of the one out of five used by Sandostatin LAR.

 

This should give better results for a longer period of time.  But that is what the study is to determine. Not publicized but very important is the side effect of shrinking existing tumors.  Many patients in stage 1 testing reported this effect.

 

It is a six month study and if it works it may just extend my life expectancy by up to two more years.  If it doesn’t work…well I’m no worse off than I was before.  The only downside to the study is daily self injections.  I’m not a fan of needles.

 

On September 7, I had my last LAR shot and am in the process of weaning myself off of the long acting drug with sub-q injections of Sandostatin.  After four weeks of this I must STOP all drugs before administering the SOM230.  That will be the rough period.  I really don’t want to go back to the experiences I am familiar with before Sandostatin.  But it will be done!

 

March 4, 2005

Update.  We started the trial of SOM230b on November 1, 2004.  We concluded on January 24, 2005.  The doctors declared that the drug was only “marginally” effective and due likely to my advanced condition, it could not do much for me.  CT scans taken before the trial and right after verified that two of the larger tumors shrank.  But another had grown.  The drug was not really that helpful to others in the trial.  Good idea, just didn’t work for me.

 

However, during the course of the treatment and trial, we learned that one of the world’s best liver surgeons, Dr. Nick N. Nissen, was working out of Cedars Sinai.  I asked our team doctors, Lim and Heaney about Nick and they not only knew him, he was very good buddies with Heaney.

 

Dr. Heaney showed Nissen my CT scans and other reports to Nissen and they discussed the case.  I was asked to meet with Nissen and when we did, imagine my surprise to learn that he thought he could help me with a resection of the liver.  He went on to state that I was strong enough to withstand the procedure and where they turn down about 8 out of 10 with a similar condition, I was one of the lucky ones they would consider.

 

To my amazement I learned that the liver will grow back, usually with several weeks.  And what grows back will be healthy!  Wow!  Why had this not been mentioned by anyone before? 

 

So on January 31, 2005 at 11:00 AM I underwent the surgery.  They removed the entire right lobe, about 65% of the total liver, then 5 tumors ranging from a tennis ball size down to golf ball size, leaving about 25% of the total liver.  (It is possible to lose up to 85% and survive.  But that is with a healthy liver).  The operation took about 4 hours and I spent 1 full week in the hospital.  Recovery is suppose to take about two months. 

 

In 3 months I will return for another treatment, Radio Frequency Ablation, a process where they insert a rather large needle into the liver, guide it into a tumor and then turn up the heat which “cooks” and kills the tumor.  They propose to do this to the one ping pong ball size tumor in the left lobe.  The remainder of the tumors, about marble size, will be left alone for now since they are too small for most procedures.

 

What a journey it has been!  From inoperable and incurable to gaining the function of my liver again!  I’m not well and I know this is not a cure but we are sure delaying the victory that Carcinoid had in mind.  My symptoms have greatly reduced and I am hopeful I will be able to return to some chores around the house in a few months. 

 


Death has not conquered!

 

I have been released!  From a body that was in decay, growing weaker, and would have given out at some point in the future anyway.

 

I have been restored!  In a new body as promised by my Lord Jesus Christ.

 

I am reconciled with my Lord for eternity.

 

I am remembered by so many loving and caring friends and family that I will continue to live in their hearts.

 

I am grateful to my God for the privilege of having a wonderful life.

 

I thank my God for the opportunity to learn and grow the way He wanted. 

 

I had many failures but only one victory was necessary and He provided that!

 

I don’t want to start a list of those I have loved and who love me, but of course the one person that cannot be ignored is Margie.  My very best friend and companion for life.  We took a vow that we lived everyday. As a result, we truly become one as God has so ordered in His Word.  All of His blessings were bestowed upon us.  No one has ever had it better than we did.

 

My life was one of complete contentment.  God filled every need.  My wife and I loved each other completely. 

 

So I ask, “How could death possibly conquer?”

 

Once again, God has the final victory.  To Him I give my life.  A poor offering indeed but it is what He asked for.

 

 

Bill Evans